Gastrointestinal autonomic nerve sarcoma presenting as a giant intra-abdominal cyst. uri icon

Overview

abstract

  • Gastrointestinal autonomic nerve sarcomas are rare tumours. A 36-year-old man presented with abdominal pain, distension and constipation. Abdominal ultrasound and CT scanning demonstrated a giant cystic intra-abdominal mass. Laparotomy confirmed a large cystic mass arising from the ileum with multiple metastases. Immunohistochemical staining was positive for vimentin, neuronal-specific enolase and PGP9.5. This is the first reported case to present as a giant intra-abdominal cyst. Specialist histopathological and immunohistochemical analysis is essential to establish the diagnosis of this rare tumour.

publication date

  • January 1, 2000

Research

keywords

  • Abdomen
  • Cysts
  • Enteric Nervous System
  • Peripheral Nervous System Neoplasms
  • Sarcoma

Identity

Scopus Document Identifier

  • 0033764254

PubMed ID

  • 11053953

Additional Document Info

volume

  • 17

issue

  • 4