Type Ia glycogenosis associated with hepatocellular carcinoma. Review uri icon

Overview

abstract

  • The predisposition of preexisting cirrhotic metabolic liver disease to the development of hepatocellular carcinoma is well established. However, the association between glycogenoses (a form of noncirrhotic metabolic liver disease) and the formation of benign and malignant liver tumors is less well known. The sixth case of simultaneous occurrence of glycogenosis type Ia and hepatocellular carcinoma, which occurred in a 34-year-old man referred for advice on therapy for his malignant neoplasm, is reported. Cases previously described in the literature are reviewed and management of this entity in light of the current knowledge in the diagnosis and treatment of hepatocellular carcinoma is discussed.

publication date

  • March 15, 1992

Research

keywords

  • Carcinoma, Hepatocellular
  • Glycogen Storage Disease Type I
  • Liver Neoplasms

Identity

Scopus Document Identifier

  • 0026586238

PubMed ID

  • 1311620

Additional Document Info

volume

  • 69

issue

  • 6