Adult-onset asthma and periocular xanthogranulomas in a patient with lymphoplasmacytic sclerosing pancreatitis. uri icon

Overview

abstract

  • The clinical syndrome of adult-onset asthma and periocular xanthogranulomas represents a rare systemic autoimmune disorder that has not been previously associated with autoimmune pancreatitis. Herein, we describe the case report of a 61-year-old man with the unique clinical association of adult-onset asthma, atopy, and periocular xanthogranulomas, who had previously been diagnosed with lymphoplasmacytic sclerosing pancreatitis. We have previously reported the case of a patient with lymphoplasmacytic sclerosing pancreatitis that developed postoperative inflammatory pseudotumor of the orbit. These unique, extrapancreatic, ocular manifestations of this disease add to the published observations that it is a systemic disorder with the potential for multiorgan involvement that may have a spectrum of clinical manifestations that includes adult-onset asthma and periocular xanthogranulomas.

publication date

  • January 1, 2007

Research

keywords

  • Asthma
  • Granuloma, Plasma Cell
  • Orbital Diseases
  • Pancreatitis
  • Xanthomatosis

Identity

Scopus Document Identifier

  • 33846032338

PubMed ID

  • 17198199

Additional Document Info

volume

  • 34

issue

  • 1