Rosai-Dorfman disease presenting as a pulmonary artery mass. uri icon

Overview

abstract

  • Rosai-Dorfman disease is rare and typically presents with cervical lymphadenopathy, but may manifest as extranodal disease. This disease is generally indolent and self-limited, but it carries a poor or fatal prognosis when it is advanced or when it involves and compresses vital structures. We present a case of Rosai-Dorfman disease affecting the pulmonary arteries in a 22-year-old woman with severe, symptomatic right heart failure.

publication date

  • January 1, 2010

Research

keywords

  • Histiocytosis, Sinus
  • Pulmonary Artery
  • Vascular Diseases
  • Vascular Surgical Procedures

Identity

Scopus Document Identifier

  • 76449089388

Digital Object Identifier (DOI)

  • 10.1016/j.athoracsur.2009.05.016

PubMed ID

  • 20103266

Additional Document Info

volume

  • 89

issue

  • 1