Congenital extrahepatic portosystemic shunt (Abernethy malformation) treated endovascularly with vascular plug shunt closure. uri icon

Overview

abstract

  • A 3-year-old boy, who presented with progressive cyanosis and hypoxia, was diagnosed with a large congenital extrahepatic portosystemic shunt, interrupted IVC with azygos continuation, and multiple congenital anomalies. Traditionally open and laparoscopic surgical techniques have been used to treat this malformation. Endovascular repair using a 16-mm Amplatzer vascular plug (AGA Medical Corporation, Golden Valley, Minnesota, USA) was used to occlude the shunt. Immediate post-placement venography demonstrated cessation of flow within the shunt and increased portal venous flow. The patient's hypoxia and cyanosis decreased significantly, and he was discharged on the 5th post-procedure day in stable clinical condition. Three months follow-up evaluation demonstrated the vascular plug in place, unchanged in position.

publication date

  • July 8, 2011

Research

keywords

  • Endovascular Procedures
  • Portacaval Shunt, Surgical
  • Portal Vein
  • Vascular Malformations
  • Vena Cava, Inferior

Identity

Scopus Document Identifier

  • 84857628621

Digital Object Identifier (DOI)

  • 10.1007/s00383-011-2944-y

PubMed ID

  • 21739127

Additional Document Info

volume

  • 28

issue

  • 1