Juvenile granulosa cell tumor associated with Maffucci syndrome in pregnancy: A case report. uri icon

Overview

abstract

  • Juvenile granulosa cell tumor (JGCT) is an extremely rare ovarian tumor that has been associated with Maffucci syndrome. It both secretes hormone and has been postulated to grow in response to hormone. We present a case of a 33-year-old G1P0 asymptomatic woman with a history of Maffucci syndrome found to have a left adnexal mass on routine ultrasonography at 13 weeks gestation. This case demonstrates the sonographic and magnetic resonance imaging (MRI) features of JGCT, as well as the natural progression of the tumor during pregnancy. A follow-up ultrasound 3 weeks after initial diagnosis demonstrated marked growth in size and vascularity of the tumor, prompting unilateral salpingo-oophorectomy. Histopathological findings confirmed the diagnosis of JGCT.

publication date

  • March 13, 2019

Research

keywords

  • Enchondromatosis
  • Granulosa Cell Tumor
  • Ovarian Neoplasms
  • Pregnancy Complications, Neoplastic

Identity

Scopus Document Identifier

  • 85063797985

Digital Object Identifier (DOI)

  • 10.1016/j.clinimag.2019.03.008

PubMed ID

  • 30965205

Additional Document Info

volume

  • 56