Abnormalities of the corrected QT interval in familial dysautonomia: an indicator of autonomic dysfunction. Academic Article uri icon

Overview

abstract

  • We report abnormalities in corrected QT intervals with changes in position and after exercise in patients with familial dysautonomia and confirm the previously reported finding of abnormal heart rate and blood pressure responses. Prolonged corrected QT intervals (> 440 msec) with lack of appropriate shortening with exercise is a noninvasive means of demonstrating an aberration in autonomic regulation of cardiac conduction.

publication date

  • June 1, 1993

Research

keywords

  • Autonomic Nervous System
  • Dysautonomia, Familial
  • Electrocardiography

Identity

Scopus Document Identifier

  • 0027287304

PubMed ID

  • 8501573

Additional Document Info

volume

  • 122

issue

  • 6